{
    "disease_id": "DOID:0070662",
    "recommended_name": {
        "id": "DOID:0070662",
        "resource": "Disease Ontology",
        "url": "https://disease-ontology.org/term/DOID:0070662",
        "name": "subcutaneous panniculitis-like T-cell lymphoma",
        "description": "A primary cutaneous T-cell non-Hodgkin lymphoma characterized by infiltration of subcutaneous tissue by neoplastic alpha-beta cytotoxic T cells mimicking panniculitis. Homozygous or compound heterozygous mutation in the HAVCR2 gene may contribute to development of this disease, with some evidence of incomplete penetrance."
    },
    "synonyms": [
        {
            "id": "DOID:0070662",
            "resource": "Disease Ontology",
            "url": "https://disease-ontology.org/term/DOID:0070662",
            "name": "SPTCL",
            "description": ""
        },
        {
            "id": "MONDO:0019475",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0019475",
            "name": "subcutaneous panniculitis-like T-cell lymphoma",
            "description": "Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a rare cytotoxic cutaneous lymphoma that has been recognized as a distinct subset of peripheral T-cell lymphomas originating and presenting primarily in the subcutaneous fat tissue."
        },
        {
            "id": "MONDO:0019475",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0019475",
            "name": "SPTCL",
            "description": ""
        },
        {
            "id": "MONDO:0019475",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0019475",
            "name": "subcutaneous panniculitic T-cell lymphoma",
            "description": ""
        },
        {
            "id": "MONDO:0019475",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0019475",
            "name": "subcutaneous panniculitis-like T-cell lymphoma",
            "description": ""
        },
        {
            "id": "MONDO:0019475",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0019475",
            "name": "subcutaneous panniculitis-like T-cell lymphoma (Alpha/Beta type)",
            "description": ""
        },
        {
            "id": "MONDO:0019475",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0019475",
            "name": "subcutaneous panniculitis-like T-cell lymphoma, Alpha/Beta type",
            "description": ""
        },
        {
            "id": "MIM:618398",
            "resource": "MIM",
            "url": "https://www.omim.org/entry/618398",
            "name": "T-cell lymphoma, subcutaneous panniculitis-like",
            "description": "T-cell lymphoma, subcutaneous panniculitis-like"
        }
    ],
    "children": [],
    "id_list": [
        "DOID:0070662"
    ],
    "unlinked_id_list": []
}
