{
    "disease_id": "DOID:0060643",
    "recommended_name": {
        "id": "DOID:0060643",
        "resource": "Disease Ontology",
        "url": "https://disease-ontology.org/term/DOID:0060643",
        "name": "primary sclerosing cholangitis",
        "description": "A sclerosing cholangitis characterized by fibroobliterative inflammation of the biliary tract, leading to cirrhosis and portal hypertension."
    },
    "synonyms": [
        {
            "id": "MONDO:0013433",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0013433",
            "name": "primary sclerosing cholangitis",
            "description": "Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure."
        },
        {
            "id": "MONDO:0013433",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0013433",
            "name": "PSC",
            "description": ""
        },
        {
            "id": "MONDO:0013433",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0013433",
            "name": "cholangitis, primary sclerosing",
            "description": ""
        }
    ],
    "children": [],
    "id_list": [
        "DOID:0060643"
    ],
    "unlinked_id_list": []
}
