{
    "disease_id": "DOID:0050158",
    "recommended_name": {
        "id": "DOID:0050158",
        "resource": "Disease Ontology",
        "url": "https://disease-ontology.org/term/DOID:0050158",
        "name": "desquamative interstitial pneumonia",
        "description": "An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation."
    },
    "synonyms": [
        {
            "id": "DOID:0050158",
            "resource": "Disease Ontology",
            "url": "https://disease-ontology.org/term/DOID:0050158",
            "name": "respiratory bronchiolitis-associated interstitial lung disease",
            "description": ""
        },
        {
            "id": "DOID:0050158",
            "resource": "Disease Ontology",
            "url": "https://disease-ontology.org/term/DOID:0050158",
            "name": "RBILD",
            "description": ""
        },
        {
            "id": "DOID:0050158",
            "resource": "Disease Ontology",
            "url": "https://disease-ontology.org/term/DOID:0050158",
            "name": "familial desquamative interstitial pneumonitis",
            "description": ""
        },
        {
            "id": "MONDO:0009887",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0009887",
            "name": "desquamative interstitial pneumonia",
            "description": "A rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis."
        },
        {
            "id": "MONDO:0009887",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0009887",
            "name": "RBILD",
            "description": ""
        },
        {
            "id": "MONDO:0009887",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0009887",
            "name": "desquamative interstitial pneumonia",
            "description": ""
        },
        {
            "id": "MONDO:0009887",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0009887",
            "name": "respiratory bronchiolitis interstitial lung disease",
            "description": ""
        },
        {
            "id": "MONDO:0009887",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0009887",
            "name": "DIP",
            "description": ""
        },
        {
            "id": "MONDO:0009887",
            "resource": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0009887",
            "name": "interstitial pneumonitis, desquamative, familial",
            "description": ""
        }
    ],
    "children": [],
    "id_list": [
        "DOID:0050158"
    ],
    "unlinked_id_list": [],
    "crossref": [
        {
            "id": "DOID:0050158",
            "database": "Disease Ontology",
            "url": "https://disease-ontology.org/term/DOID:0050158",
            "categories": []
        },
        {
            "id": "MONDO:0009887",
            "database": "MONDO",
            "url": "https://monarchinitiative.org/disease/MONDO:0009887",
            "categories": []
        }
    ],
    "proteins": [
        {
            "uniprot_canonical_ac": "P21841-1",
            "uniprot_ac": "P21841",
            "uniprot_id": "PSPC_MOUSE",
            "refseq_ac": "",
            "glycoprotein": "no",
            "species": [
                {
                    "name": "Mus musculus",
                    "taxid": 10090,
                    "common_name": "Mouse",
                    "glygen_name": "Mouse",
                    "reference_species": "Mus musculus [10090]"
                }
            ],
            "protein_names": [
                {
                    "name": "Surfactant protein C",
                    "type": "recommended"
                },
                {
                    "name": "Pulmonary surfactant-associated protein C",
                    "type": "synonym"
                },
                {
                    "name": "Pulmonary surfactant-associated proteolipid SPL(Val)",
                    "type": "synonym"
                },
                {
                    "name": "SP-C",
                    "type": "synonym"
                },
                {
                    "name": "SP5",
                    "type": "synonym"
                }
            ],
            "gene_names": [
                {
                    "name": "Sftpc",
                    "type": "recommended"
                },
                {
                    "name": "Sftp2",
                    "type": "synonym"
                }
            ],
            "record_id": "P21841-1",
            "evidence": [
                {
                    "id": "0050158",
                    "database": "AGR",
                    "url": "https://www.alliancegenome.org/disease/DOID:0050158"
                }
            ]
        },
        {
            "uniprot_canonical_ac": "P11685-1",
            "uniprot_ac": "P11685",
            "uniprot_id": "PSPC_RAT",
            "refseq_ac": "NP_059038",
            "glycoprotein": "no",
            "species": [
                {
                    "name": "Rattus norvegicus",
                    "taxid": 10116,
                    "common_name": "Rat",
                    "glygen_name": "Rat",
                    "reference_species": "Rattus norvegicus [10116]"
                }
            ],
            "protein_names": [
                {
                    "name": "Surfactant protein C",
                    "type": "recommended"
                },
                {
                    "name": "Pulmonary surfactant-associated protein C",
                    "type": "synonym"
                },
                {
                    "name": "Pulmonary surfactant-associated proteolipid SPL(Val)",
                    "type": "synonym"
                },
                {
                    "name": "SP-C",
                    "type": "synonym"
                },
                {
                    "name": "Surfactant, pulmonary-associated protein C",
                    "type": "synonym"
                },
                {
                    "name": "pulmonary surfactant-associated protein C",
                    "type": "synonym"
                },
                {
                    "name": "pulmonary surfactant-associated proteolipid SPL(Val)",
                    "type": "synonym"
                },
                {
                    "name": "surfactant associated protein C",
                    "type": "synonym"
                },
                {
                    "name": "surfactant protein C",
                    "type": "synonym"
                }
            ],
            "gene_names": [
                {
                    "name": "Sftpc",
                    "type": "recommended"
                },
                {
                    "name": "SP-C",
                    "type": "synonym"
                },
                {
                    "name": "Sftp2",
                    "type": "synonym"
                },
                {
                    "name": "Sftpc",
                    "type": "synonym"
                }
            ],
            "record_id": "P11685-1",
            "evidence": [
                {
                    "id": "0050158",
                    "database": "AGR",
                    "url": "https://www.alliancegenome.org/disease/DOID:0050158"
                }
            ]
        },
        {
            "uniprot_canonical_ac": "O15520-1",
            "uniprot_ac": "O15520",
            "uniprot_id": "FGF10_HUMAN",
            "refseq_ac": "NP_004456",
            "glycoprotein": "yes",
            "species": [
                {
                    "name": "Homo sapiens",
                    "taxid": 9606,
                    "common_name": "Human",
                    "glygen_name": "Human",
                    "reference_species": "Homo sapiens [9606]"
                }
            ],
            "protein_names": [
                {
                    "name": "Fibroblast growth factor 10",
                    "type": "recommended"
                },
                {
                    "name": "FGF-10",
                    "type": "synonym"
                },
                {
                    "name": "Keratinocyte growth factor 2",
                    "type": "synonym"
                },
                {
                    "name": "fibroblast growth factor 10 precursor",
                    "type": "synonym"
                },
                {
                    "name": "keratinocyte growth factor 2",
                    "type": "synonym"
                },
                {
                    "name": "produced by fibroblasts of urinary bladder lamina propria",
                    "type": "synonym"
                }
            ],
            "gene_names": [
                {
                    "name": "FGF10",
                    "type": "recommended"
                },
                {
                    "name": "FGF10",
                    "type": "synonym"
                },
                {
                    "name": "LADD3",
                    "type": "synonym"
                }
            ],
            "record_id": "O15520-1",
            "evidence": [
                {
                    "id": "0050158",
                    "database": "AGR",
                    "url": "https://www.alliancegenome.org/disease/DOID:0050158"
                }
            ]
        },
        {
            "uniprot_canonical_ac": "P11686-1",
            "uniprot_ac": "P11686",
            "uniprot_id": "PSPC_HUMAN",
            "refseq_ac": "NP_001165828",
            "glycoprotein": "no",
            "species": [
                {
                    "name": "Homo sapiens",
                    "taxid": 9606,
                    "common_name": "Human",
                    "glygen_name": "Human",
                    "reference_species": "Homo sapiens [9606]"
                }
            ],
            "protein_names": [
                {
                    "name": "Surfactant protein C",
                    "type": "recommended"
                },
                {
                    "name": "BRICHOS domain containing 6",
                    "type": "synonym"
                },
                {
                    "name": "Pulmonary surfactant-associated protein C",
                    "type": "synonym"
                },
                {
                    "name": "Pulmonary surfactant-associated proteolipid SPL(Val)",
                    "type": "synonym"
                },
                {
                    "name": "SP-C",
                    "type": "synonym"
                },
                {
                    "name": "SP5",
                    "type": "synonym"
                },
                {
                    "name": "pulmonary surfactant apoprotein-2 SP-C",
                    "type": "synonym"
                },
                {
                    "name": "pulmonary surfactant-associated proteolipid SPL(Val)",
                    "type": "synonym"
                },
                {
                    "name": "surfactant protein C isoform 2",
                    "type": "synonym"
                }
            ],
            "gene_names": [
                {
                    "name": "SFTPC",
                    "type": "recommended"
                },
                {
                    "name": "BRICD6",
                    "type": "synonym"
                },
                {
                    "name": "PSP-C",
                    "type": "synonym"
                },
                {
                    "name": "SFTP2",
                    "type": "synonym"
                },
                {
                    "name": "SFTPC",
                    "type": "synonym"
                },
                {
                    "name": "SMDP2",
                    "type": "synonym"
                },
                {
                    "name": "SP-C",
                    "type": "synonym"
                }
            ],
            "record_id": "P11686-1",
            "evidence": [
                {
                    "id": "0050158",
                    "database": "AGR",
                    "url": "https://www.alliancegenome.org/disease/DOID:0050158"
                }
            ]
        }
    ],
    "glycans": [],
    "biomarkers": [],
    "association_flag": "1000",
    "record_id": "doid.0050158"
}